Reduction of globotriaosylceramide in Fabry disease mice by substrate deprivation (Q28507844)

24 January 2017

title

Reduction of globotriaosylceramide in Fabry disease mice by substrate deprivation (English)

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24 January 2017

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GOA release 2020-03-11

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A. Abe

1

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24 January 2017

S. Gregory

2

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24 January 2017

L. Lee

3

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24 January 2017

P. D. Killen

4

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24 January 2017

R. O. Brady

5

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24 January 2017

A. Kulkarni

6

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24 January 2017

J. A. Shayman

7

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24 January 2017

language of work or name

English

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publication date

1 June 2000

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Journal of Clinical Investigation

24 January 2017

published in

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24 January 2017

volume

105

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24 January 2017

issue

11

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24 January 2017

page(s)

1563–1571

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A genetic model of substrate deprivation therapy for a glycosphingolipid storage disorder

24 January 2017

cites work

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alpha-Galactosidase A deficient mice: a model of Fabry disease

19 March 2017

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19 March 2017

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19 March 2017

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Glycosphingolipid depletion in fabry disease lymphoblasts with potent inhibitors of glucosylceramide synthase

19 March 2017

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Infusion of alpha-galactosidase A reduces tissue globotriaosylceramide storage in patients with Fabry disease

29 September 2017

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29 September 2017

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29 September 2017

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29 September 2017

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Cell cycle arrest induced by an inhibitor of glucosylceramide synthase. Correlation with cyclin-dependent kinases

2 June 2018

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Structural and stereochemical studies of potent inhibitors of glucosylceramide synthase and tumor cell growth.

2 June 2018

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2 June 2018

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Metabolism of D-[3H]threo-1-phenyl-2-decanoylamino-3-morpholino-1-propanol, an inhibitor of glucosylceramide synthesis, and the synergistic action of an inhibitor of microsomal monooxygenase

2 June 2018

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Rapid kidney changes resulting from glycosphingolipid depletion by treatment with a glucosyltransferase inhibitor

2 June 2018

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2 June 2018

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Improved Inhibitors of Glucosylceramide Synthase

2 June 2018

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12 December 2020

Inhibitors of glucosylceramide synthase

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12 December 2020

Inhibitors and stimulators of glucocerebroside metabolism

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12 December 2020

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12 December 2020

Extensive Glycosphingolipid Depletion in the Liver and Lymphoid Organs of Mice Treated withN-Butyldeoxynojirimycin

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12 December 2020

Ceramide glycanase from rat mammary tissues: inhibition by PPMP(D-/L-) and its probable role in signal transduction

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12 December 2020

A unique glycosphingolipid-splitting enzyme (ceramide-glycanase from leech) cleaves the linkage between the oligosaccharide and the ceramide

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12 December 2020

Aging and food restriction: effect on lipids of cerebral cortex

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12 December 2020