ALS-associated mutations in TDP-43 increase its stability and promote TDP-43 complexes with FUS/TLS. (Q34068067)

30 July 2017

title

ALS-associated mutations in TDP-43 increase its stability and promote TDP-43 complexes with FUS/TLS. (English)

1 reference

amyotrophic lateral sclerosis

30 July 2017

main subject

1 reference

based on heuristic

inferred from title

author

Clotilde Lagier-Tourenne

4

object named as

Clotilde Lagier-Tourenne

0 references

Don W. Cleveland

7

object named as

Don W Cleveland

1 reference

30 July 2017

Shuo-Chien Ling

1

1 reference

30 July 2017

Claudio P Albuquerque

2

1 reference

30 July 2017

Joo Seok Han

3

1 reference

30 July 2017

Seiya Tokunaga

5

1 reference

30 July 2017

Huilin Zhou

6

1 reference

30 July 2017

language of work or name

English

0 references

publication date

12 July 2010

1 reference

Proceedings of the National Academy of Sciences of the United States of America

30 July 2017

published in

1 reference

30 July 2017

volume

107

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30 July 2017

issue

30

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30 July 2017

page(s)

13318-13323

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TDP-43 and FUS/TLS: emerging roles in RNA processing and neurodegeneration

30 July 2017

cites work

1 reference

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Global analysis of TDP-43 interacting proteins reveals strong association with RNA splicing and translation machinery.

5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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TDP-43 overexpression enhances exon 7 inclusion during the survival of motor neuron pre-mRNA splicing

5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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TDP-43, the signature protein of FTLD-U, is a neuronal activity-responsive factor

5 July 2018

1 reference

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5 July 2018

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5 July 2018

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5 July 2018

1 reference

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5 July 2018

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Depletion of TDP 43 overrides the need for exonic and intronic splicing enhancers in the human apoA-II gene.

5 July 2018

1 reference

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TDP-43 binds heterogeneous nuclear ribonucleoprotein A/B through its C-terminal tail: an important region for the inhibition of cystic fibrosis transmembrane conductance regulator exon 9 splicing

5 July 2018

1 reference

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5 July 2018

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1 reference

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1 reference

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1 reference

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1 reference

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1 reference

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1 reference

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1 reference

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1 reference

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5 July 2018

1 reference

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1 reference

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5 July 2018

1 reference

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TDP-43 redistribution is an early event in sporadic amyotrophic lateral sclerosis.

28 October 2018

1 reference

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28 October 2018

Identifiers

DOI

10.1073/PNAS.1008227107

1 reference

30 July 2017

0 references

1 reference

30 July 2017

1 reference