Distinct structural and mechanical properties of the nuclear lamina in Hutchinson-Gilford progeria syndrome (Q34772038)

4 August 2017

title

Distinct structural and mechanical properties of the nuclear lamina in Hutchinson-Gilford progeria syndrome (English)

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4 August 2017

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6

Tom Misteli

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4 August 2017

Kris Noel Dahl

1

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4 August 2017

Paola Scaffidi

2

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4 August 2017

Mohammad F Islam

3

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4 August 2017

Arjun G Yodh

4

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4 August 2017

Katherine L Wilson

5

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4 August 2017

language of work or name

English

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publication date

26 June 2006

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Proceedings of the National Academy of Sciences of the United States of America

4 August 2017

published in

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4 August 2017

volume

103

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4 August 2017

issue

27

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4 August 2017

page(s)

10271-10276

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Progressive vascular smooth muscle cell defects in a mouse model of Hutchinson-Gilford progeria syndrome

4 August 2017

cites work

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Integrity matters: linking nuclear architecture to lifespan

7 July 2018

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Incomplete processing of mutant lamin A in Hutchinson-Gilford progeria leads to nuclear abnormalities, which are reversed by farnesyltransferase inhibition

7 July 2018

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Abnormal nuclear shape and impaired mechanotransduction in emerin-deficient cells

7 July 2018

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Power-law rheology of isolated nuclei with deformation mapping of nuclear substructures

7 July 2018

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Genomic instability in laminopathy-based premature aging

7 July 2018

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Reversal of the cellular phenotype in the premature aging disease Hutchinson-Gilford progeria syndrome

7 July 2018

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The nuclear lamina comes of age.

7 July 2018

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Nuclear envelope breakdown requires overcoming the mechanical integrity of the nuclear lamina

7 July 2018

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Accumulation of mutant lamin A causes progressive changes in nuclear architecture in Hutchinson-Gilford progeria syndrome

7 July 2018

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Lamin A/C deficiency causes defective nuclear mechanics and mechanotransduction.

7 July 2018

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Recurrent de novo point mutations in lamin A cause Hutchinson–Gilford progeria syndrome

7 July 2018

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Lamin a truncation in Hutchinson-Gilford progeria.

7 July 2018

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Spatial microstimuli in endothelial mechanosignaling

7 July 2018

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Lamins: building blocks or regulators of gene expression?

7 July 2018

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Life at the edge: the nuclear envelope and human disease

7 July 2018

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Nuclear lamins: building blocks of nuclear architecture

7 July 2018

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Nuclear pore complexes form immobile networks and have a very low turnover in live mammalian cells

7 July 2018

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Lamins in disease: why do ubiquitously expressed nuclear envelope proteins give rise to tissue-specific disease phenotypes?

7 July 2018

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Essential roles for Caenorhabditis elegans lamin gene in nuclear organization, cell cycle progression, and spatial organization of nuclear pore complexes

7 July 2018

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High mobility of proteins in the mammalian cell nucleus

7 July 2018

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Dynamics of the nuclear lamina as monitored by GFP-tagged A-type lamins.

7 July 2018

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The Hutchinson-Gilford progeria syndrome. Report of 4 cases and review of the literature

7 July 2018

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Nuclear protein import in permeabilized mammalian cells requires soluble cytoplasmic factors

7 July 2018

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A lamin-independent pathway for nuclear envelope assembly

7 July 2018

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The nuclear envelope lamina network has elasticity and a compressibility limit suggestive of a molecular shock absorber

7 July 2018

1 reference

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Searching for clues to premature aging

26 October 2018

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12 December 2020

Increased solubility of lamins and redistribution of lamin C in X-linked Emery-Dreifuss muscular dystrophy fibroblasts

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12 December 2020

The application of a homogeneous half-space model in the analysis of endothelial cell micropipette measurements

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12 December 2020

In vitro reconstitution of recombinant lamin A and a lamin A mutant lacking the carboxy-terminal tail

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12 December 2020

Here come the SUNs: a nucleocytoskeletal missing link

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12 December 2020

Identifiers

DOI

10.1073/PNAS.0601058103

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4 August 2017

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4 August 2017

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