Deletion of C9ORF72 results in motor neuron degeneration and stress sensitivity in C. elegans (Q35070967)

6 August 2017

title

Deletion of C9ORF72 results in motor neuron degeneration and stress sensitivity in C. elegans (English)

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6 August 2017

main subject

Caenorhabditis elegans

0 references

2

Guy A Rouleau

0 references

Patrick A Dion

series ordinal

3

object named as

Patrick A Dion

1 reference

6 August 2017

1

Martine Therrien

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6 August 2017

J Alex Parker

4

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6 August 2017

language of work or name

English

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publication date

12 December 2013

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6 August 2017

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6 August 2017

volume

8

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6 August 2017

issue

12

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6 August 2017

page(s)

e83450

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Creative Commons Attribution 4.0 International

6 August 2017

copyright license

start time

12 December 2013

1 reference

April 2022 Public Data File from Crossref

copyright status

copyrighted

0 references

cites work

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8 July 2018

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Hypermethylation of the CpG island near the G4C2 repeat in ALS with a C9orf72 expansion

8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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Unconventional translation of C9ORF72 GGGGCC expansion generates insoluble polypeptides specific to c9FTD/ALS

8 July 2018

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The C9orf72 GGGGCC repeat is translated into aggregating dipeptide-repeat proteins in FTLD/ALS.

8 July 2018

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The product of C9orf72, a gene strongly implicated in neurodegeneration, is structurally related to DENN Rab-GEFs

8 July 2018

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Caenorhabditis elegans RNA-processing protein TDP-1 regulates protein homeostasis and life span

8 July 2018

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8 July 2018

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A hexanucleotide repeat expansion in C9ORF72 is the cause of chromosome 9p21-linked ALS-FTD

8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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Hypertonic stress induces rapid and widespread protein damage in C. elegans

8 July 2018

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8 July 2018

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Mutations in FUS, an RNA processing protein, cause familial amyotrophic lateral sclerosis type 6

8 July 2018

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Mutations in the FUS/TLS gene on chromosome 16 cause familial amyotrophic lateral sclerosis

8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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8 July 2018

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Multiple sequence alignment with the Clustal series of programs

8 July 2018

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Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

8 July 2018

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RNA binding mediates neurotoxicity in the transgenic Drosophila model of TDP-43 proteinopathy

8 July 2018

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Loss of function of C9orf72 causes motor deficits in a zebrafish model of amyotrophic lateral sclerosis.

27 September 2018

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Pharmacological reduction of ER stress protects against TDP-43 neuronal toxicity in vivo.

27 September 2018

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An RNAi screen identifies genes that regulate GABA synapses

27 September 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3861484

Analysis of synaptic transmission in Caenorhabditis elegans using an aldicarb-sensitivity assay.

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3861484

Too salty for worms: hypertonic stress challenges proteostasis networks. Focus on “Hypertonic stress induces rapid and widespread protein damage in C. elegans”

27 September 2018

1 reference

Crossref

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0083450

10.1371/JOURNAL.PONE.0083450

21 January 2018

Identifiers

DOI

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6 August 2017

0 references

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6 August 2017

1 reference