Human and animal models of V(D)J recombination deficiency (Q35538187)

8 August 2017

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title

Human and animal models of V(D)J recombination deficiency (English)

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8 August 2017

author

Jean-Pierre de Villartay

1

object named as

Jean-Pierre de Villartay

0 references

Gwenaël Le Guyader

object named as

Gwenaël Le Guyader

5

1 reference

ORCID Public Data File 2021

author name string

Jean-Pierre de Villartay

1

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8 August 2017

Catherine Poinsignon

2

1 reference

8 August 2017

Regina de Chasseval

3

1 reference

8 August 2017

Dietke Buck

4

1 reference

8 August 2017

Isabelle Villey

6

1 reference

8 August 2017

publication date

1 October 2003

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Current Opinion in Immunology

8 August 2017

published in

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8 August 2017

volume

15

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8 August 2017

issue

5

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8 August 2017

page(s)

592-598

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The mechanism and regulation of chromosomal V(D)J recombination

8 August 2017

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RAG-2-deficient mice lack mature lymphocytes owing to inability to initiate V(D)J rearrangement

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Identical mutations in RAG1 or RAG2 genes leading to defective V(D)J recombinase activity can cause either T-B-severe combined immune deficiency or Omenn syndrome

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VDJ recombination: a transposase goes to work

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The V(D)J recombinase efficiently cleaves and transposes signal joints

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In vivo transposition mediated by V(D)J recombinase in human T lymphocytes

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7 January 2021

The C-terminal portion of RAG2 protects against transposition in vitro

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7 January 2021

Regulation of RAG1/RAG2-mediated transposition by GTP and the C-terminal region of RAG2

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7 January 2021

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7 January 2021

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7 January 2021

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7 January 2021

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7 January 2021

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7 January 2021

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7 January 2021

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Identifiers

DOI

1 reference

8 August 2017

1 reference