Uncoordinated transcription and compromised muscle function in the lmna-null mouse model of Emery- Emery-Dreyfuss muscular dystrophy. (Q33834124)

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24 January 2020

title

Uncoordinated transcription and compromised muscle function in the lmna-null mouse model of Emery- Emery-Dreyfuss muscular dystrophy (English)

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24 January 2020

2

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Robert B. White

6

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24 January 2020

Yin-Biao Sun

8

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Peter S Zammit

10

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author name string

Viola F Gnocchi

1

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Zhe Huang

3

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24 January 2020

Ken Brady

4

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24 January 2020

Jaclyn S Lee

5

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Jennifer E Morgan

7

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Juliet A Ellis

9

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language of work or name

English

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publication date

22 February 2011

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24 January 2020

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24 January 2020

volume

6

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issue

2

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page(s)

e16651

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Creative Commons Attribution 4.0 International

24 January 2020

copyright license

start time

22 February 2011

1 reference

April 2022 Public Data File from Crossref

copyright status

copyrighted

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cites work

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28 July 2018

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28 July 2018

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28 July 2018

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28 July 2018

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28 July 2018

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28 July 2018

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28 July 2018

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28 July 2018

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28 July 2018

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28 July 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Impaired nuclear functions lead to increased senescence and inefficient differentiation in human myoblasts with a dominant p.R545C mutation in the LMNA gene

21 January 2018

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21 January 2018

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Modifications in myotendinous junction surface morphology in dystrophin-deficient mouse muscle

21 January 2018

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Chromatin changes induced by lamin A/C deficiency and the histone deacetylase inhibitor trichostatin A.

21 January 2018

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Skeletal and cardiac muscle defects in a murine model of Emery-Dreifuss muscular dystrophy

29 October 2018

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29 October 2018

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29 October 2018

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21 January 2018

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Mouse model carrying H222P- Lmna mutation develops muscular dystrophy and dilated cardiomyopathy similar to human striated muscle laminopathies

21 January 2018

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12 December 2020

Culturing satellite cells from living single muscle fiber explants

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12 December 2020

The lethal phenotype of a homozygous nonsense mutation in the lamin A/C gene

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12 December 2020

Gamma irradiation prevents compensatory hypertrophy of overloaded mouse extensor digitorum longus muscle

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12 December 2020

The epigenetics of nuclear envelope organization and disease

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12 December 2020

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12 December 2020

Myonuclear degeneration in LMNA null mice

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12 December 2020

10.1371/JOURNAL.PONE.0016651

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21364987%20AND%20SRC:MED&resulttype=core&format=json

24 January 2020

0 references

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21364987%20AND%20SRC:MED&resulttype=core&format=json

24 January 2020

PubMed publication ID

21364987

1 reference