Systematically perturbed folding patterns of amyotrophic lateral sclerosis (ALS)-associated SOD1 mutants (Q33895940)

29 July 2017

title

Systematically perturbed folding patterns of amyotrophic lateral sclerosis (ALS)-associated SOD1 mutants (English)

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amyotrophic lateral sclerosis

29 July 2017

main subject

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4

Peter M Andersen

1 reference

29 July 2017

Mikael J Lindberg

1

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29 July 2017

Roberth Byström

series ordinal

2

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29 July 2017

Niklas Boknäs

series ordinal

3

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29 July 2017

Mikael Oliveberg

series ordinal

5

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29 July 2017

language of work or name

English

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publication date

29 June 2005

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Proceedings of the National Academy of Sciences of the United States of America

29 July 2017

published in

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29 July 2017

volume

102

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29 July 2017

issue

28

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29 July 2017

page(s)

9754-9759

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Small-molecule-mediated stabilization of familial amyotrophic lateral sclerosis-linked superoxide dismutase mutants against unfolding and aggregation

29 July 2017

cites work

1 reference

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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Cu/Zn superoxide dismutase mutants associated with amyotrophic lateral sclerosis show enhanced formation of aggregates in vitro

5 July 2018

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The structure of holo and metal-deficient wild-type human Cu, Zn superoxide dismutase and its relevance to familial amyotrophic lateral sclerosis

5 July 2018

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5 July 2018

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5 July 2018

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Common denominator of Cu/Zn superoxide dismutase mutants associated with amyotrophic lateral sclerosis: decreased stability of the apo state

5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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Unspecific hydrophobic stabilization of folding transition states

5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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Aggregation and Motor Neuron Toxicity of an ALS-Linked SOD1 Mutant Independent from Wild-Type SOD1

5 July 2018

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5 July 2018

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Diffusion control in an elementary protein folding reaction

5 July 2018

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Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

5 July 2018

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Amyotrophic lateral sclerosis and structural defects in Cu,Zn superoxide dismutase

5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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Dissociation of human copper-zinc superoxide dismutase dimers using chaotrope and reductant. Insights into the molecular basis for dimer stability

29 October 2018

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29 October 2018

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29 October 2018

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Monomeric Cu,Zn-superoxide dismutase is a common misfolding intermediate in the oxidation models of sporadic and familial amyotrophic lateral sclerosis.

29 October 2018

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Complete change of the protein folding transition state upon circular permutation.

29 October 2018

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Mutant Cu/Zn-superoxide dismutase proteins have altered solubility and interact with heat shock/stress proteins in models of amyotrophic lateral sclerosis

29 October 2018

1 reference

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How do small single-domain proteins fold?

29 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1174986

Aggregation of mutant Cu/Zn superoxide dismutase proteins in a culture model of ALS

29 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1174986

Mutations in SOD1 associated with amyotrophic lateral sclerosis cause novel protein interactions

29 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1174986

Purification of human recombinant superoxide dismutase by isoelectric focusing in a multicompartment electrolyzer with zwitterionic membranes.

29 October 2018

1 reference

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Role of the tertiary and quaternary structures in the stability of dimeric copper, zinc superoxide dismutases

29 October 2018

1 reference

12 December 2020

Time scale of protein aggregation dictated by liquid-liquid demixing

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12 December 2020

Sixteen novel mutations in the Cu/Zn superoxide dismutase gene in amyotrophic lateral sclerosis: a decade of discoveries, defects and disputes

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12 December 2020

SOD1 aggregates in ALS: cause, correlate or consequence?

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12 December 2020

Folding by association

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12 December 2020

Evidence of stable monomeric species in the unfolding of Cu,Zn superoxide dismutase from Photobacterium leiognathi

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12 December 2020

Islet amyloid polypeptide-induced membrane leakage involves uptake of lipids by forming amyloid fibers

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12 December 2020

The unusually stable quaternary structure of human Cu,Zn-superoxide dismutase 1 is controlled by both metal occupancy and disulfide status

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12 December 2020

Identifiers

DOI

10.1073/PNAS.0501957102

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29 July 2017

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29 July 2017

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