Duchenne's muscular dystrophy: animal models used to investigate pathogenesis and develop therapeutic strategies (Q35591025)

9 August 2017

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title

Duchenne's muscular dystrophy: animal models used to investigate pathogenesis and develop therapeutic strategies (English)

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9 August 2017

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C A Collins

1

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9 August 2017

J E Morgan

series ordinal

2

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9 August 2017

publication date

1 August 2003

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International Journal of Experimental Pathology

9 August 2017

published in

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9 August 2017

volume

84

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9 August 2017

issue

4

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9 August 2017

page(s)

165-172

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Restoration of dystrophin expression in mdx muscle cells by chimeraplast-mediated exon skipping

9 August 2017

cites work

1 reference

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Dystrophic phenotype of canine X-linked muscular dystrophy is mitigated by adenovirus-mediated utrophin gene transfer.

15 November 2018

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Zebrafish: from disease modeling to drug discovery.

15 November 2018

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High-efficiency plasmid gene transfer into dystrophic muscle

15 November 2018

1 reference

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The dystrophin associated protein complex in zebrafish

15 November 2018

1 reference

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Non-viral gene delivery in skeletal muscle: a protein factory

15 November 2018

1 reference

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Dystrophin-glycoprotein complex: post-translational processing and dystroglycan function.

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Enhanced dystrophic progression in mdx mice by exercise and beneficial effects of taurine and insulin-like growth factor-1.

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Prevention of pathology in mdx mice by expression of utrophin: analysis using an inducible transgenic expression system.

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Remission of clinical signs in early duchenne muscular dystrophy on intermittent low-dosage prednisolone therapy

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Oligonucleotide-mediated gene therapy for muscular dystrophies

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Current protocol of a research phase I clinical trial of full-length dystrophin plasmid DNA in Duchenne/Becker muscular dystrophies. Part I: rationale.

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Viral vectors for gene transfer of micro-, mini-, or full-length dystrophin

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Gene transfer studies in animals: what do they really tell us about the prospects for gene therapy in DMD?

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Stable micro-dystrophin gene transfer using an integrating adeno-retroviral hybrid vector ameliorates the dystrophic pathology in mdx mouse muscle.

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Efficacy of myoblast transplantation in nonhuman primates following simple intramuscular cell injections: toward defining strategies applicable to humans

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Utrophin binds laterally along actin filaments and can couple costameric actin with sarcolemma when overexpressed in dystrophin-deficient muscle

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Muscle lesions associated with dystrophin deficiency in neonatal golden retriever puppies

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Comparative evolution of muscular dystrophy in diaphragm, gastrocnemius and masseter muscles from old male mdx mice

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Harnessing the potential of dystrophin-related proteins for ameliorating Duchenne's muscular dystrophy

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

The dystrophin / utrophin homologues in Drosophila and in sea urchin

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Muscular dystrophy: the worm turns to genetic disease

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Prevention of the dystrophic phenotype in dystrophin/utrophin-deficient muscle following adenovirus-mediated transfer of a utrophin minigene

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Progress in myoblast transplantation: a potential treatment of dystrophies

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

In vitro interactions of Caenorhabditis elegans dystrophin with dystrobrevin and syntrophin.

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Molecular analysis of a spontaneous dystrophin 'knockout' dog.

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Dystrobrevin- and dystrophin-like mutants display similar phenotypes in the nematode Caenorhabditis elegans.

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Mutations in the Caenorhabditis elegans dystrophin-like gene dys-1 lead to hyperactivity and suggest a link with cholinergic transmission

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

High-level dystrophin expression after adenovirus-mediated dystrophin minigene transfer to skeletal muscle of dystrophic dogs: prolongation of expression with immunosuppression.

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Use of the dog model for Duchenne muscular dystrophy in gene therapy trials.

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Myoblast implantation in Duchenne muscular dystrophy: the San Francisco study.

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Deficiency of merosin in dystrophic dy mice and genetic linkage of laminin M chain gene to dy locus

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Tarsal joint contracture in dogs with golden retriever muscular dystrophy

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Murine muscular dystrophy caused by a mutation in the laminin alpha 2 (Lama2) gene

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Long-term persistence and migration of myogenic cells injected into pre-irradiated muscles of mdx mice

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

X chromosome-linked muscular dystrophy (mdx) in the mouse

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Dystrophin: the protein product of the Duchenne muscular dystrophy locus

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Canine X-linked muscular dystrophy. An animal model of Duchenne muscular dystrophy: clinical studies

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Conversion of mdx myofibres from dystrophin-negative to -positive by injection of normal myoblasts

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Normal myogenic cells from newborn mice restore normal histology to degenerating muscles of the mdx mouse

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

A New Immunodeficient Mouse Model for Human Myoblast Transplantation

15 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2517561

Cardiomyopathy in dystrophin-deficient hypertrophic feline muscular dystrophy

15 November 2018

1 reference

12 December 2020

Myoblast transplantation in whole muscle of nonhuman primates

1 reference

12 December 2020

In vivo targeted repair of a point mutation in the canine dystrophin gene by a chimeric RNA/DNA oligonucleotide

1 reference

12 December 2020

T-cell-dependent fibrosis in the mdx dystrophic mouse

1 reference

12 December 2020

Development of muscle pathology in canine X-linked muscular dystrophy. II. Quantitative characterization of histopathological progression during postnatal skeletal muscle development

1 reference

12 December 2020

Dystrophin in adult zebrafish muscle

1 reference

12 December 2020

Changes of skeletal muscle in young dystrophin-deficient cats: a morphological and morphometric study

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12 December 2020

The worm in us - Caenorhabditis elegans as a model of human disease

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12 December 2020

Tibialis anterior muscles in mdx mice are highly susceptible to contraction-induced injury

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12 December 2020

Fibrogenic cytokines and extent of fibrosis in muscle of dogs with X-linked golden retriever muscular dystrophy

1 reference

12 December 2020

Canine X-linked muscular dystrophy in Japan (CXMDJ)

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12 December 2020

Muscle development in mdx mutant mice

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12 December 2020

Skeletal muscle pathology in X chromosome-linked muscular dystrophy (mdx) mouse

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12 December 2020

Muscle precursor cells invade and repopulate freeze-killed muscles

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12 December 2020

Normal myoblast injections provide genetic treatment for murine dystrophy

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12 December 2020

The homologue of the Duchenne locus is defective in X-linked muscular dystrophy of dogs

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12 December 2020

The mdx mouse skeletal muscle myopathy: II. Contractile properties

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12 December 2020

Ultrastructure of the skeletal muscle in the X chromosome-linked dystrophic (mdx) mouse. Comparison with Duchenne muscular dystrophy

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12 December 2020

Mdx muscle grafts retain the mdx phenotype in normal hosts

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12 December 2020

[Muscular dystrophy in a cat]

1 reference

12 December 2020

Expression of utrophin (dystrophin-related protein) during regeneration and maturation of skeletal muscle in canine X-linked muscular dystrophy

1 reference

12 December 2020

Low-dose prednisolone treatment in Duchenne and Becker muscular dystrophy

1 reference

12 December 2020

Expression of truncated utrophin leads to major functional improvements in dystrophin-deficient muscles of mice

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12 December 2020

10.1046/J.1365-2613.2003.00354.X

Identifiers

DOI

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9 August 2017

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