Novel antibodies reveal inclusions containing non-native SOD1 in sporadic ALS patients (Q33996210)

30 July 2017

title

Novel antibodies reveal inclusions containing non-native SOD1 in sporadic ALS patients (English)

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amyotrophic lateral sclerosis

30 July 2017

main subject

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1 reference

3

Peter M Andersen

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30 July 2017

Karin Forsberg

1

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30 July 2017

P Andreas Jonsson

2

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30 July 2017

Daniel Bergemalm

4

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30 July 2017

Karin S Graffmo

5

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30 July 2017

Magnus Hultdin

6

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30 July 2017

Johan Jacobsson

7

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30 July 2017

Roland Rosquist

8

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30 July 2017

Stefan L Marklund

9

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30 July 2017

Thomas Brännström

10

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30 July 2017

language of work or name

English

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publication date

14 July 2010

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30 July 2017

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30 July 2017

volume

5

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30 July 2017

issue

7

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30 July 2017

page(s)

e11552

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Creative Commons Attribution 4.0 International

30 July 2017

copyright license

start time

14 July 2010

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April 2022 Public Data File from Crossref

copyright status

copyrighted

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cites work

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5 July 2018

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Conversion to the amyotrophic lateral sclerosis phenotype is associated with intermolecular linked insoluble aggregates of SOD1 in mitochondria

5 July 2018

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Systematically perturbed folding patterns of amyotrophic lateral sclerosis (ALS)-associated SOD1 mutants

5 July 2018

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Gait analysis detects early changes in transgenic SOD1(G93A) mice

5 July 2018

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Unraveling the mechanisms involved in motor neuron degeneration in ALS

5 July 2018

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Misfolded CuZnSOD and amyotrophic lateral sclerosis

5 July 2018

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New consensus research on neuropathological aspects of familial amyotrophic lateral sclerosis with superoxide dismutase 1 (SOD1) gene mutations: inclusions containing SOD1 in neurons and astrocytes.

5 July 2018

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Caspase-1 and -3 are sequentially activated in motor neuron death in Cu,Zn superoxide dismutase-mediated familial amyotrophic lateral sclerosis

5 July 2018

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Slowing of axonal transport is a very early event in the toxicity of ALS-linked SOD1 mutants to motor neurons

5 July 2018

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Aggregation and Motor Neuron Toxicity of an ALS-Linked SOD1 Mutant Independent from Wild-Type SOD1

5 July 2018

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Familial amyotrophic lateral sclerosis with a mutation in exon 4 of the Cu/Zn superoxide dismutase gene: pathological and immunocytochemical changes

5 July 2018

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Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury

5 July 2018

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Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

5 July 2018

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Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation

5 July 2018

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Extracellular superoxide dismutase in human tissues and human cell lines

5 July 2018

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Superoxide dismutase in amyotrophic lateral sclerosis patients homozygous for the D90A mutation

5 July 2018

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Clinicopathological phenotype of ALS with a novel G72C SOD1 gene mutation mimicking a myopathy

29 October 2018

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Monomeric Cu,Zn-superoxide dismutase is a common misfolding intermediate in the oxidation models of sporadic and familial amyotrophic lateral sclerosis.

29 October 2018

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Minute quantities of misfolded mutant superoxide dismutase-1 cause amyotrophic lateral sclerosis

29 October 2018

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29 October 2018

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29 October 2018

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Human Cu/Zn superoxide dismutase (SOD1) overexpression in mice causes mitochondrial vacuolization, axonal degeneration, and premature motoneuron death and accelerates motoneuron disease in mice expressing a familial amyotrophic lateral sclerosis mut

29 October 2018

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Amyotrophic lateral sclerosis associated with genetic abnormalities in the gene encoding Cu/Zn superoxide dismutase: molecular pathology of five new cases, and comparison with previous reports and 73 sporadic cases of ALS.

29 October 2018

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29 October 2018

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29 October 2018

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Intense superoxide dismutase-1 immunoreactivity in intracytoplasmic hyaline inclusions of familial amyotrophic lateral sclerosis with posterior column involvement

29 October 2018

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Natural history of amyotrophic lateral sclerosis in a database population Validation of a scoring system and a model for survival prediction

29 October 2018

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Rapid disease progression correlates with instability of mutant SOD1 in familial ALS

29 October 2018

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Immunocytochemical study of the distribution of the free radical scavenging enzymes CU/ZN superoxide dismutase (SOD1); MN superoxide dismutase (MN SOD) and catalase in the normal human spinal cord and in motor neuron disease

29 October 2018

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12 December 2020

Normal Binding and Reactivity of Copper in Mutant Superoxide Dismutase Isolated from Amyotrophic Lateral Sclerosis Patients

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12 December 2020

Coincident thresholds of mutant protein for paralytic disease and protein aggregation caused by restrictively expressed superoxide dismutase cDNA

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12 December 2020

Disulphide-reduced superoxide dismutase-1 in CNS of transgenic amyotrophic lateral sclerosis models

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12 December 2020

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12 December 2020

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12 December 2020

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12 December 2020

Presymptomatic motor neuron loss and reactive astrocytosis in the SOD1 mouse model of amyotrophic lateral sclerosis

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12 December 2020

Sixteen novel mutations in the Cu/Zn superoxide dismutase gene in amyotrophic lateral sclerosis: a decade of discoveries, defects and disputes

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12 December 2020

Papers from the 3rd International Symposium on Amyotrophic Lateral Sclerosis/Motor Neurone Disease. Genetics and Cell Biology of the Motor Neurone. Birmingham, United Kingdom, November 2-4, 1992

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12 December 2020

Cu/Zn superoxide dismutase-like immunoreactivity in Lewy body-like inclusions of sporadic amyotrophic lateral sclerosis

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12 December 2020

Superoxide dismutase concentration and activity in familial amyotrophic lateral sclerosis

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12 December 2020

Amyotrophic lateral sclerosis associated with homozygosity for an Asp90Ala mutation in CuZn-superoxide dismutase

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12 December 2020

10.1371/JOURNAL.PONE.0011552

Identifiers

DOI

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30 July 2017

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30 July 2017

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